Liver disease after Fontan procedure

Liver disease related to Fontan’s surgery is a structural and functional liver disease after performing the Fontan procedure. As in other liver diseases, the course can be progressive, potentially leading to the appearance of complications, such as cirrhosis, ascites, esophageal varices or encephalopathy. Its origin is not inflammatory, but congestive. Among the complementary tests, the Doppler ultrasound, elastography and liver biopsy stand out. Its treatment is multidisciplinary, and includes optimizing cardiac function, prevention and management of liver complications, and prevention of fatty liver disease.