Acute hemorrhagic edema of infancy; a disorder not very well known

The acute hemorrhagic edema of infancy (AHEI) is an unusual variant of leukocitoclastic vasculitis affecting infants and children up to three years of age. Clinically it is characterised by a large palpable purpura with a dramatic appearance but an usually benign course. We present an infant with AHEI and compare this disorder with the Schonlein-Henoch purpura.