Headache with atypical features

Headache is a frequent reason for consultation and it has experienced an increase in its incidence in recent years. In most cases, they are primary headaches that do not require additional studies. However, it is essential to exclude those which are originated by an underlying cause, paying attention to possible warning signs. We here present the case of a two-and-a-half-year-old child with repeated episodes of headache with atypical features, with a limited response to initial treatment. In some cases, the symptoms associated with headache can be subtle, making it difficult to recognize them. Benign epileptic disorders exist, such as the Panayiotopoulos Syndrome which is characterized by seizures with predominance of autonomic symptoms, which can associate headache. It is important to know this syndrome in order to be able to recognize the symptoms and carry out an adequate diagnosis and treatment.