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Vol. 17 - Num. 65

Clinical Reviews

Tolosa-Hunt syndrome, a diagnosis of exclusion

M.ª Isabel Buedo Rubioa, María del Pilar Martín-Tamayo Blázquezb, I Onsurbe Ramírezb

aServicio de Pediatría. Complejo Hospitalario Universitario de Albacete. Albacete. España.
bUnidad de Neuropediatría. Servicio de Pediatría. Complejo Hospitalario Universitario de Albacete. Albacete. España.

Correspondence: MI Buedo. E-mail: mibuedor@sescam.jccm.es

Reference of this article: Buedo Rubio MI, Martín-Tamayo Blázquez MP, Onsurbe Ramírez I. Tolosa-Hunt syndrome, a diagnosis of exclusion. Rev Pediatr Aten Primaria. 2015;17:e45-e47.

Published in Internet: 13-03-2015 - Visits: 21663

Abstract

Painful ophthalmoplegia is a rare entity in children, characterized by orbital pain and ipsilateral oculomotor paresis. The Tolosa-Hunt syndrome (THS), is caused by a granulomatous inflammation involving the cavernous sinus or superior orbital fissure of unknown etiology.

The diagnosis of THS is based upon the clinical presentation in conjunction with neuroimaging results. The STH usually has good clinical response to corticosteroids, but occasionally ophthalmoplegia persists in varying degrees and some patients follow a relapsing-remitting course.

Keywords

Painful opthalmoplegia Tolosa-Hunt syndrome

 

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