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Clinical Reviews

Possible PHACE(S) syndrome

Authors:

Jiménez Castillo MIa, Moleón Rodríguez FJb, Martín Masot Rc

aPediatra. CS Almanjayar. Granada. España.
bMIR-MFyC. CS Cartuja. Granada. España .
cMIR-Pediatría. Hospital Materno Infantil Virgen de las Nieves. Granada. España.

Correspondence: MI Jiménez. Email: inesjc2005@hotmail.com

Reference of this article.:

Jiménez Castillo MI, Moleón Rodríguez FJ, Martín Masot R. Posible síndrome de PHACE(S). Rev Pediatr Aten Primaria. 2017;19:51-6.

Published in Internet: 10/01/2017

Abstract:

Infantile hemangiomas are a frequent reason for consultation in Pediatrics. When extensive cutaneous hemangiomas are observed and specially if they affect the face, we we should suspect a neurocutaneous disorder called PHACE(S) syndrome. Diagnosis must be based on clinical criteria in order to evaluate and treat possible complications that sometimes can be lethal. A proper management of the patients requires a multidisciplinary intervention, with the purpose of reducing stress and preventing the ocurrence of complications of the hemangioma and the disorders associated to the syndrome.Beta-blockers are employed as first-line treatment of cutaneous hemangiomas, but in these patients a prior screening of possible cerebrovascular and cardiac malformations is needed. Endocrine alterations are rare, so a high diagnostic suspicion is required to avoid going unnoticed.

Keywords: Skin abnormalities. Stroke. Cerebral arterial diseases. Cerebral infarction. Dandy-Walker. Hemangioma.


 


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ISSN 2174-4106  Publicación Open Acess, incluida en DOAJ, sin cargo por publicación.

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