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Vol. 23 - Num. 89

Clinical Reviews

Intravascular papillary endothelial hyperplasia in the supraclavicular region

Aída M.ª Gutiérrez Sáncheza, Ana Calabuig Adobesa, Gema Carmen Marcéna, Natalia Estrada Mallarinob, Ainara González Esquedac, Carmelo Guerrero Laleonaa

aServicio de Pediatría. Hospital Infantil Universitario Miguel Servet. Zaragoza. España.
bServicio de Anatomía Patológica. Hospital Universitario Miguel Servet. Zaragoza. España.
cServicio de Cirugía Pediátrica. Hospital Universitario Miguel Servet. Zaragoza. España.

Correspondence: AM Gutiérrez. E-mail: amgsjm@gmail.com

Reference of this article: Gutiérrez Sánchez AM, Calabuig Adobes A, Carmen Marcén G, Estrada Mallarino N, González Esqueda A, Guerrero Laleona C. Intravascular papillary endothelial hyperplasia in the supraclavicular region. Rev Pediatr Aten Primaria. 2021;23:87-90.

Published in Internet: 30-03-2021 - Visits: 5054

Abstract

Intravascular papillary endothelial hyperplasia (IPEH) is a rare benign vascular lesion that usually presents as a nonspecific erythematous-violaceous subcutaneous neoformation. The histopathological study, necessary for the confirmatory diagnosis, shows papillary proliferation of endothelial cells associated with thrombotic material. IPEH can simulate other lesions such as angiosarcoma, so the correct diagnosis of this entity is essential to avoid aggressive treatments. The resection with wide margins is usually enough.

Keywords

Benign vascular lesion Intravascular papillary endothelial hyperplasia Masson's tumor

 

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